Abstract
Isolated pulmonary involvement in Langerhans Cell Histiocytosis (LCH) is rare in childhood. The authors report a 6-y- old boy presenting with recurrent pneumothorax, whose CT thorax showed diffuse pulmonary cystic lucencies bilaterally. Biopsy of the lesions confirmed pulmonary LCH with Cd1a and S 100 positivity.
MeSH terms
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Antigens, CD1 / metabolism
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Child
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Fatal Outcome
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Histiocytosis, Langerhans-Cell / complications
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Histiocytosis, Langerhans-Cell / diagnosis*
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Histiocytosis, Langerhans-Cell / diagnostic imaging
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Histiocytosis, Langerhans-Cell / metabolism
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Histiocytosis, Langerhans-Cell / therapy
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Humans
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Immunohistochemistry
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Male
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Pleurodesis
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Pneumothorax / diagnostic imaging
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Pneumothorax / etiology
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Recurrence
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S100 Proteins / metabolism
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Tomography, X-Ray Computed
Substances
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Antigens, CD1
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CD1a antigen
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S100 Proteins