Abstract
Systemic vasculitides are inflammatory diseases of blood vessels of various sizes, which mechanisms are different according to diseases. Classification can be made according to vessel size, histology and pathogenesis. Giant cell arteritis comprises Horton's disease and Takayasu's arteritis. Different mechanisms have been individualized in the group of necrotizing vasculitides: some are associated with ANCA and other to immune complexes. Other mechanisms have not been yet identified. One of the major purposes of classification is to describe adequately diseases and their outcome, then to treat them appropriately.
Copyright © 2012 Elsevier Masson SAS. All rights reserved.
MeSH terms
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Adult
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Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / classification
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Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / diagnosis
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Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis / etiology
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Antibodies, Antineutrophil Cytoplasmic / analysis
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Antibodies, Antineutrophil Cytoplasmic / immunology
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Antigens / immunology
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Child
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Diagnosis, Differential
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Humans
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Models, Biological
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Serologic Tests
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Systemic Vasculitis / classification*
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Systemic Vasculitis / diagnosis
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Systemic Vasculitis / epidemiology
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Takayasu Arteritis / classification
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Takayasu Arteritis / diagnosis
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Takayasu Arteritis / immunology
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Takayasu Arteritis / pathology
Substances
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Antibodies, Antineutrophil Cytoplasmic
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Antigens