Background: Craniopharyngioma is a rare fetal and neonatal tumor.
Case report: We report a case of a congenital craniopharyngioma diagnosed by prenatal magnetic resonance. This diagnosis was confirmed by postnatal MR imaging, neurosurgical treatment and histopathological examination.
Conclusions: Outcome of neonatal craniopharyngioma is very poor, even if radical surgery is performed. The main problems are pituitary insufficiency, diabetes insipidus, and visual disturbance.
Keywords: congenital brain tumor; craniopharyngioma; fetus; magnetic resonance imaging.