Abstract
Autoimmune synaptic encephalitis (ASE) is a recently recognized disease entity. The early and correct diagnosis of ASE is of importance, since the prognosis depends on the early onset of treatment. We present two Danish case reports of ASE: a 15-year-old boy presenting with a severe course of N-methyl-D-aspartate-encephalitis including persistent cognitive deficits, and a 59-year-old woman with coeliac disease presenting with leucine-rich glioma inactivated 1-encephalitis including dyskinesia, epilepsy, psychiatric features and vocal tics.
MeSH terms
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Adolescent
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Anti-N-Methyl-D-Aspartate Receptor Encephalitis* / complications
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Anti-N-Methyl-D-Aspartate Receptor Encephalitis* / diagnosis
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Anti-N-Methyl-D-Aspartate Receptor Encephalitis* / therapy
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Autoantibodies / blood
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Autoimmune Diseases of the Nervous System* / complications
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Autoimmune Diseases of the Nervous System* / diagnosis
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Autoimmune Diseases of the Nervous System* / therapy
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Denmark
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Female
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Humans
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Intracellular Signaling Peptides and Proteins
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Limbic Encephalitis* / complications
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Limbic Encephalitis* / diagnosis
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Limbic Encephalitis* / therapy
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Magnetic Resonance Imaging
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Male
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Mental Disorders / etiology
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Middle Aged
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Proteins / immunology
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Receptors, N-Methyl-D-Aspartate / immunology
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Synapses* / immunology
Substances
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Autoantibodies
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Intracellular Signaling Peptides and Proteins
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LGI1 protein, human
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Proteins
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Receptors, N-Methyl-D-Aspartate