Myocardial contraction and long QT syndrome

Abstract

The long QT syndrome is an inherited cardiac arrhythmic disease that has been regarded as a purely electrical disease. However, sporadic reports have indicated that myocardial contraction abnormalities are present in these patients. Novel echocardiographic techniques such as strain echocardiography have made it possible to further elucidate cardiac mechanics in patients with long QT syndrome. Here, we provide an overview of current reports on myocardial mechanical alterations in patients with long QT syndrome.