Cutaneous vasculitis associated with pheochromocytoma

Arthritis Rheum. 1990 Dec;33(12):1852-6. doi: 10.1002/art.1780331215.

Abstract

We describe a patient who presented with constitutional symptoms, severe hypertension, and purpuric lesions over the knees, thighs, and penis. The patient was eventually diagnosed as having multiple endocrine neoplasia type II, with cutaneous leukocytoclastic vasculitis. The cutaneous vasculitis persisted despite treatment with high-dose systemic corticosteroids, but rapidly resolved after the removal of bilateral pheochromocytomas. This case demonstrates cutaneous leukocytoclastic vasculitis in association with pheochromocytoma.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Adrenal Gland Neoplasms / complications*
  • Adrenal Gland Neoplasms / diagnosis
  • Adrenal Gland Neoplasms / pathology
  • Adult
  • Humans
  • Male
  • Pheochromocytoma / complications*
  • Pheochromocytoma / diagnosis
  • Pheochromocytoma / pathology
  • Tomography, X-Ray Computed
  • Vasculitis, Leukocytoclastic, Cutaneous / complications*
  • Vasculitis, Leukocytoclastic, Cutaneous / drug therapy
  • Vasculitis, Leukocytoclastic, Cutaneous / pathology

Substances

  • Adrenal Cortex Hormones