[Molecular mechanisms for the improvement of wound healing ability of periodontal ligament in Marfan's syndrome]

Clin Calcium. 2012 Jan;22(1):35-42.
[Article in Japanese]

Abstract

Marfan's syndrome (MFS) is a systemic disorder of the connective tissues caused by insufficient fibrillin-1 microfibril formation and can cause cardiac complications, emphysema, ocular lens dislocation and severe periodontal disease. ADAMTSL6β, a microfibril-associated extracellular matrix protein that has been implicated in fibrillin-1 microfibril assembly is able to improve microfibril insufficiency in MFS mice model. These findings suggest a new therapeutic strategy for the treatment of MFS through ADAMTSL6β-mediated fibrillin-1 microfibril assembly. We here review effect on ADAMTSL6β to the improvement of microfibril insufficiency in periodontal tissue as a model.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Extracellular Matrix Proteins / physiology*
  • Fibrillin-1
  • Fibrillins
  • Humans
  • Marfan Syndrome / genetics*
  • Marfan Syndrome / physiopathology*
  • Marfan Syndrome / therapy
  • Mice
  • Microfibrils / metabolism
  • Microfibrils / physiology*
  • Microfilament Proteins / physiology
  • Molecular Targeted Therapy
  • Periodontal Ligament / physiopathology*
  • Protein Multimerization
  • Regeneration
  • Wound Healing / genetics*

Substances

  • Extracellular Matrix Proteins
  • FBN1 protein, human
  • Fbn1 protein, mouse
  • Fibrillin-1
  • Fibrillins
  • Microfilament Proteins