Isolated type a interrupted aortic arch: in an asymptomatic 19-year-old man

Tex Heart Inst J. 2011;38(5):559-61.

Abstract

Interrupted aortic arch, characterized by luminal and anatomic discontinuity between the ascending and descending aorta, is a very rare congenital malformation. The condition is typically diagnosed in neonates and is highly fatal if left untreated. Herein, we report the unusual diagnosis of an isolated type A interrupted aortic arch in a hypertensive, asymptomatic 19-year-old man.

Keywords: Adult; aorta, thoracic/abnormalities/radiography; aortic arch syndromes/congenital/epidemiology/pathology; heart defects, congenital/radiography.

Publication types

  • Case Reports

MeSH terms

  • Aorta, Thoracic / abnormalities*
  • Aortography / methods
  • Asymptomatic Diseases
  • Humans
  • Hypertension / complications
  • Hypertension / diagnosis
  • Male
  • Predictive Value of Tests
  • Tomography, X-Ray Computed
  • Vascular Malformations / complications
  • Vascular Malformations / diagnosis*
  • Young Adult