Contribution of anti-ryanodine receptor antibody to impairment of excitation-contraction coupling in myasthenia gravis

Clin Neurophysiol. 2012 Jun;123(6):1242-7. doi: 10.1016/j.clinph.2011.10.038. Epub 2011 Dec 1.

Abstract

Objective: The aim of this study was to elucidate the relationship between the impairment of excitation-contraction (E-C) coupling and anti-ryanodine receptor (RyR) antibody in patients with myasthenia gravis (MG).

Methods: Masseteric compound muscle action potential (CMAP) and mandibular movement-related potentials (MRPs) were recorded simultaneously after stimulating the trigeminal motor nerve with a needle electrode. The E-C coupling time (ECCT) was calculated as the latency difference between CMAP and MRP. For each patient, we selected a representative data set when there was no abnormal decrement in response to repetitive nerve stimulation. The 26 data sets were divided into an anti-RyR-positive group (n=12) and an anti-RyR-negative group (n=14).

Results: Masseteric ECCT was significantly longer (p=0.017) in anti-RyR-positive group (median, mean, range; 3.6, 3.8, 3.0-5.9 ms) than in anti-RyR-negative group (3.1, 3.1, 2.7-4.0) although there were no significant differences in masseteric CMAP amplitude and % decrement between the two groups. The bite force was significantly lower in anti-RyR-positive group than in normal controls.

Conclusions: Presence of anti-RyR antibodies is associated with significantly prolonged masseteric ECCT compared to absence of the antibodies in MG.

Significance: Anti-RyR antibody contributes to E-C coupling impairment in the masseter muscle in patients with MG.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Action Potentials / immunology
  • Adult
  • Aged
  • Autoantibodies / blood*
  • Bite Force
  • Excitation Contraction Coupling / immunology*
  • Female
  • Humans
  • Male
  • Middle Aged
  • Muscle Weakness / immunology
  • Muscle Weakness / physiopathology*
  • Myasthenia Gravis / immunology
  • Myasthenia Gravis / physiopathology*
  • Ryanodine Receptor Calcium Release Channel / immunology*

Substances

  • Autoantibodies
  • Ryanodine Receptor Calcium Release Channel