Abstract
Up to 5% of all diagnosed colorectal cancers has a hereditary cuase. Colon cancer arise in younger individuals, and extracolonic tumors are also frequent. A precise understanding of main syndromes will allow the proper management of these patients, including genetic counselling, screening and prophylactic surgery.
Copyright © 2011 Elsevier España, S.L. All rights reserved.
MeSH terms
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Adenomatous Polyposis Coli / diagnosis
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Adenomatous Polyposis Coli / epidemiology
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Adenomatous Polyposis Coli / genetics
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Adenomatous Polyposis Coli / therapy
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Anti-Inflammatory Agents, Non-Steroidal / therapeutic use
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Anticarcinogenic Agents / therapeutic use
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Colectomy
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Colonoscopy
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Colorectal Neoplasms / diagnosis
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Colorectal Neoplasms / epidemiology
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Colorectal Neoplasms / genetics*
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Colorectal Neoplasms / prevention & control
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Colorectal Neoplasms / therapy
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Colorectal Neoplasms, Hereditary Nonpolyposis / diagnosis
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Colorectal Neoplasms, Hereditary Nonpolyposis / epidemiology
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Colorectal Neoplasms, Hereditary Nonpolyposis / genetics
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Colorectal Neoplasms, Hereditary Nonpolyposis / therapy
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DNA Repair / genetics
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Early Diagnosis
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Female
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Genes, APC
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Genes, Neoplasm
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Genetic Counseling
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Genital Neoplasms, Female / epidemiology
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Genital Neoplasms, Female / genetics
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Humans
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Male
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Microsatellite Instability
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Neoplasms, Multiple Primary
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Neoplastic Syndromes, Hereditary* / diagnosis
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Neoplastic Syndromes, Hereditary* / epidemiology
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Neoplastic Syndromes, Hereditary* / genetics
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Neoplastic Syndromes, Hereditary* / therapy
Substances
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Anti-Inflammatory Agents, Non-Steroidal
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Anticarcinogenic Agents