Alveolar capillary dysplasia with anorectal anomaly

Indian Pediatr. 2011 Oct;48(10):803-4.

Abstract

Alveolar capillary dysplasia (ACD) is an uncommon cause of irreversible persistent pulmonary hypertension in full-term newborn. In ACD there is a failure of formation of air - blood barrier in addition to misalignment of pulmonary veins. The etiology of the disease is still not understood. We present a case report of a full-term newborn with ACD associated with anorectal anomaly.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Anorectal Malformations
  • Anus, Imperforate / complications*
  • Anus, Imperforate / diagnosis
  • Fatal Outcome
  • Histocytochemistry
  • Humans
  • Infant, Newborn
  • Male
  • Persistent Fetal Circulation Syndrome / complications*
  • Persistent Fetal Circulation Syndrome / diagnosis
  • Pulmonary Alveoli / abnormalities

Supplementary concepts

  • Alveolar capillary dysplasia