Osteogenesis imperfecta, multiple intra-abdominal arterial dissections and a ruptured dissecting-type intracranial aneurysm

Interv Neuroradiol. 2011 Sep;17(3):371-5. doi: 10.1177/159101991101700315. Epub 2011 Oct 17.

Abstract

We describe an adult patient with a ruptured dissecting-type superior cerebellar artery aneurysm and known osteogenesis imperfecta. He was successfully treated with coil embolization and intentional parent vessel sacrifice. During his hospital admission, he also suffered from abdominal distension. An incidental note was made of multiple intra-abdominal arterial dissections. These were managed conservatively. We review the rare association of osteogenesis imperfecta and intracranial aneurysms, as well as discuss management implications.

Publication types

  • Case Reports

MeSH terms

  • Aneurysm, Ruptured / complications
  • Aneurysm, Ruptured / diagnostic imaging
  • Aneurysm, Ruptured / therapy
  • Aortic Dissection / complications
  • Aortic Dissection / diagnostic imaging
  • Aortic Dissection / therapy
  • Cerebellum / blood supply
  • Cerebral Angiography
  • Embolization, Therapeutic
  • Humans
  • Intracranial Aneurysm / complications*
  • Intracranial Aneurysm / diagnostic imaging*
  • Intracranial Aneurysm / therapy
  • Male
  • Mesenteric Artery, Superior / diagnostic imaging*
  • Middle Aged
  • Osteogenesis Imperfecta / complications*
  • Posterior Cerebral Artery / diagnostic imaging*
  • Tomography, X-Ray Computed