No abstract available
MeSH terms
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Acetylglucosaminidase / metabolism
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Brain / metabolism
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Friedreich Ataxia / metabolism*
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Gangliosides / metabolism
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Glycosaminoglycans / urine
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Humans
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Lysosomes / enzymology*
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Mannosidases / metabolism
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alpha-Galactosidase / metabolism
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alpha-Glucosidases / metabolism
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beta-Galactosidase / metabolism
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beta-Glucosidase / metabolism
Substances
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Gangliosides
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Glycosaminoglycans
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Mannosidases
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alpha-Glucosidases
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beta-Glucosidase
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alpha-Galactosidase
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beta-Galactosidase
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Acetylglucosaminidase