Aortic root vasculitis associated with Cogan's syndrome

Ann Thorac Surg. 2011 Jul;92(1):340-1. doi: 10.1016/j.athoracsur.2010.12.068.

Abstract

Cogan's syndrome is characterized by nonsyphilitic interstitial keratitis and an audiovestibular disorder resembling Meniere disease. We report a patient with progressive congestive heart failure due to massive aortic and mitral insufficiency coupled with aortitis leading to an ascending aortic aneurysm. The patient underwent successful aortic root replacement and mitral valve repair.

Publication types

  • Case Reports

MeSH terms

  • Aortic Aneurysm, Thoracic / complications
  • Aortic Aneurysm, Thoracic / diagnostic imaging
  • Aortic Aneurysm, Thoracic / surgery*
  • Aortic Valve Insufficiency / complications
  • Aortic Valve Insufficiency / diagnostic imaging
  • Aortic Valve Insufficiency / surgery*
  • Aortitis / complications
  • Aortitis / diagnosis
  • Aortitis / pathology*
  • Blood Vessel Prosthesis Implantation / methods
  • Cogan Syndrome / complications
  • Cogan Syndrome / diagnosis*
  • Echocardiography, Doppler / methods
  • Female
  • Follow-Up Studies
  • Heart Failure / complications
  • Heart Failure / diagnosis
  • Heart Valve Prosthesis Implantation / methods
  • Humans
  • Immunohistochemistry
  • Middle Aged
  • Mitral Valve Insufficiency / complications
  • Mitral Valve Insufficiency / diagnostic imaging
  • Mitral Valve Insufficiency / surgery*
  • Risk Assessment
  • Stroke Volume
  • Treatment Outcome