Abstract
Congenital pulmonary valvular dysplasia is an unusual condition typically associated with Noonan syndrome. Among its other cardiac manifestations, occasional patients with Noonan syndrome have been demonstrated to have hypertrophic nonobstructive cardiomyopathy, which may be biventricular. We report a unique case of pulmonary valvular dysplasia, dynamic right ventricular outflow tract obstruction and profound right ventricular hypertrophy with only mild left ventricular hypertrophy, in a patient without Noonan syndrome.
© 2011 Wiley Periodicals, Inc.
MeSH terms
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Coronary Angiography
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Heart Defects, Congenital / complications*
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Heart Defects, Congenital / diagnosis
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Heart Defects, Congenital / therapy
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Humans
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Hypertrophy, Left Ventricular / complications
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Hypertrophy, Left Ventricular / diagnosis
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Hypertrophy, Right Ventricular / complications*
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Hypertrophy, Right Ventricular / diagnosis
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Hypertrophy, Right Ventricular / therapy
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Magnetic Resonance Imaging
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Male
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Middle Aged
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Pulmonary Valve / abnormalities*
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Ventricular Outflow Obstruction / complications*
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Ventricular Outflow Obstruction / diagnosis
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Ventricular Outflow Obstruction / therapy