Prion seeded conversion and amplification assays

Top Curr Chem. 2011:305:121-33. doi: 10.1007/128_2011_184.

Abstract

The conversion of the normal prion protein (PrP(C)) into its misfolded, aggregation-prone and infectious (prion) isoform is central to the progression of transmissible spongiform encephalopathies (TSEs) or prion diseases. Since the initial development of a cell free PrP conversion reaction, striking progress has been made in the development of much more continuous prion-induced conversion and amplification reactions. These studies have provided major insights into the molecular underpinnings of prion propagation and enabled the development of ultra-sensitive tests for prions and prion disease diagnosis. This chapter will provide an overview of such reactions and the practical and fundamental consequences of their development.

Publication types

  • Review

MeSH terms

  • Animals
  • Biological Assay / methods*
  • Biomedical Research / trends
  • Genetic Techniques
  • Humans
  • PrPC Proteins / metabolism
  • PrPSc Proteins / metabolism
  • Prion Diseases / metabolism*
  • Prions / chemistry*
  • Protein Folding
  • Recombinant Proteins / chemistry
  • Time Factors

Substances

  • PrPC Proteins
  • PrPSc Proteins
  • Prions
  • Recombinant Proteins