Frosted branch angiitis, neuroretinitis as initial ocular manifestation in Behçet disease

Indian J Ophthalmol. 2011 May-Jun;59(3):240-1. doi: 10.4103/0301-4738.81048.

Abstract

Behçet disease is an idiopathic, multisystem disorder characterized by recurrent episodes of orogenital ulceration and vasculitis of the veins and arteries of all calibers. Ocular involvement may affect the conjunctiva, sclera, uveal tract, vitreous, blood vessels, and retina. Many theories have pointed toward an autoimmune response behind its pathogenesis, which may be triggered by exposure to an infectious agent. Frosted branch angiitis is characterized by vascular inflammation, sheathing, retinal edema, and retinal hemorrhages. The disease may be idiopathic in a majority of the cases or may be associated with ocular and systemic pathology. Association between Behηet disease, Frosted branch angiitis, and neuroretinitis is not reported in literature. This uncommon combination reflects the varied systemic and ocular manifestations in Behçet disease, especially in patients who are not diagnosed and treated in time. We hereby report a case of bilateral frosted branch angiitis and neuroretinitis in a young male from Middle-east, suffering from Behçet disease.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Antirheumatic Agents / administration & dosage
  • Behcet Syndrome / complications*
  • Behcet Syndrome / diagnosis
  • Behcet Syndrome / drug therapy
  • Colchicine / administration & dosage
  • Drug Administration Schedule
  • Fundus Oculi
  • Humans
  • Injections, Intravenous
  • Magnetic Resonance Imaging
  • Male
  • Prednisone / administration & dosage
  • Prednisone / analogs & derivatives
  • Retinal Hemorrhage / diagnosis
  • Retinal Hemorrhage / etiology
  • Retinitis / diagnosis
  • Retinitis / etiology*
  • Silymarin / administration & dosage
  • Vasculitis / diagnosis
  • Vasculitis / etiology*
  • Vasculitis / pathology*

Substances

  • Antirheumatic Agents
  • Silymarin
  • Colchicine
  • Prednisone