L-β-N-oxalyl-α,β-diaminopropionic acid toxicity in motor neurons

Neuroreport. 2011 Feb 16;22(3):131-5. doi: 10.1097/wnr.0b013e3283433027.

Abstract

The excitatory amino acid L-β-N-oxalyl-α,β-diaminopropionic acid (L-β-ODAP) in Lathyrus sativus L. is proposed as the causative agent of the neurodegenerative disease neurolathyrism. We investigated the effect of L-β-ODAP on [Ca2+]i handling, redox homeostasis, and cell death in rat spinal motor neurons. L-β-ODAP and L-glutamate triggered [Ca2+]i transients, which were inhibited by the α-amino-3-hydroxy-5-methyl-4-isoxazole propionic acid receptor blockers; 2,3-dioxo-6-nitro-1,2,3, 4-tetrahydrobenzo[f]quinoxaline-7-sulfonamide and 1-naphthyl acetylspermine, the latter specifically blocking Ca2+-permeable α-amino-3-hydroxy-5-methyl-4-isoxazole propionic acid receptors. In addition, 2,3-dioxo-6-nitro-1,2,3,4-tetrahydrobenzo[f]quinoxaline-7-sulfonamide, and to a lesser extent 1-naphthyl acetylspermine, protected the neurons against cell death induced by L-β-ODAP or L-glutamate. Methionine and cysteine were also protective against neuronal cell death. We conclude that deregulation of [Ca2+]i homeostasis and oxidative stress contribute to motor neuron cell death in neurolathyrism.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cells, Cultured
  • Lathyrism / chemically induced*
  • Lathyrism / metabolism
  • Lathyrism / pathology
  • Motor Neuron Disease / chemically induced*
  • Motor Neuron Disease / metabolism
  • Motor Neuron Disease / pathology
  • Motor Neurons / drug effects*
  • Motor Neurons / metabolism
  • Motor Neurons / pathology
  • Nerve Degeneration / chemically induced
  • Nerve Degeneration / metabolism
  • Nerve Degeneration / physiopathology
  • Oxidative Stress / drug effects
  • Oxidative Stress / physiology
  • Rats
  • beta-Alanine / analogs & derivatives*
  • beta-Alanine / toxicity

Substances

  • 3-N-oxalyl-L -2,3-diaminopropanoic acid
  • beta-Alanine