Sarcoidosis with cutaneous granulomatous vasculitis

Australas J Dermatol. 2010 Aug;51(3):198-201. doi: 10.1111/j.1440-0960.2010.00630.x.

Abstract

Ulceration of non-caseating granulomas is a rare cutaneous presentation of sarcoidosis. Granulomatous vasculitis is classically associated with Wegener's granulomatosis, lymphomatoid granulomatosis or Churg-Strauss syndrome. It is also commonly noted in pulmonary sarcoidosis, but has seldom been reported in cutaneous sarcoidosis, particularly the ulcerative variant. We present a rare case of sarcoidosis with multiple purpuric leg ulcers showing a granulomatous vasculitis histologically.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Azathioprine / therapeutic use
  • Granuloma, Giant Cell / diagnosis*
  • Granuloma, Giant Cell / drug therapy
  • Granuloma, Giant Cell / pathology
  • Humans
  • Leg Ulcer / diagnosis*
  • Leg Ulcer / drug therapy
  • Leg Ulcer / pathology
  • Male
  • Prednisolone / therapeutic use
  • Sarcoidosis / diagnosis*
  • Sarcoidosis / drug therapy
  • Sarcoidosis / pathology
  • Systemic Vasculitis / diagnosis*
  • Systemic Vasculitis / drug therapy
  • Systemic Vasculitis / pathology
  • Testicular Diseases / diagnosis
  • Testicular Diseases / drug therapy
  • Testicular Diseases / pathology

Substances

  • Prednisolone
  • Azathioprine