[Plexiform neurofibroma of the ileum and mesentery: an uncommon manifestation of neurofibromatosis type I]

Abstract

Plexiform neurofibroma is a tumor of the nerve trunks and their branches; it is considered virtually pathognomic of neurofibromatosis type 1. We present the case of a patient with neurofibromatosis type 1 and a plexiform neurofibroma involving the ileum and mesentery. This case is interesting because intestinal involvement by neurofibroma is rare and because the patient presented with symptomatic intestinal involvement that required surgery.