A Case of Kikuchi's Disease Presenting with Unique Facial Involvement

Ann Dermatol. 2010 May;22(2):196-8. doi: 10.5021/ad.2010.22.2.196. Epub 2010 May 18.

Abstract

Kikuchi's disease (KD), or histiocytic necrotizing lymphadenitis, is a rare, self-limited lymphadenopathy, typically in young women, that usually remits spontaneously and does not recur. KD is clinically characterized by cervical lymphadenopathy and a high fever. Extranodal involvement (skin, arthritis, meningitis) rarely occurs. When KD is involved in a skin lesion, it presents with various shapes, but rarely manifests with symmetrically distributed, erythematous, firm nodules only on the face. In this report, we describe a patient with KD and unique skin manifestations.

Keywords: Cutaneous involvement; Histiocytic necrotizing lymphadenitis; Kikuchi's disease.

Publication types

  • Case Reports