Leiomyosarcoma of the inferior vena cava

Medicina (Kaunas). 2010;46(3):200-3.

Abstract

Leiomyosarcoma is a rare tumor of mesenchymal origin usually affecting the inferior vena cava. Early diagnosis is essential before surgical resection, which is the only therapeutic modality that prolongs patients' survival. Ultrasonography, computer tomography, and magnetic resonance imaging are the main imaging modalities in this case. Combined with guided biopsies, they form the mainstay of reliable diagnosis. We report a case with retroperitoneal tumor arising from the middle segment of the inferior vena cava. Radiological examination revealed retroperitoneal tumor and helped to choose surgical treatment. Histopathological examination confirmed the diagnosis of leiomyosarcoma of the inferior vena cava.

Publication types

  • Case Reports

MeSH terms

  • Biopsy
  • Blood Vessel Prosthesis
  • Female
  • Follow-Up Studies
  • Humans
  • Leiomyosarcoma* / diagnosis
  • Leiomyosarcoma* / diagnostic imaging
  • Leiomyosarcoma* / pathology
  • Leiomyosarcoma* / surgery
  • Liver / pathology
  • Liver Neoplasms / diagnostic imaging
  • Liver Neoplasms / pathology
  • Liver Neoplasms / secondary
  • Magnetic Resonance Imaging
  • Radiography, Abdominal
  • Retroperitoneal Neoplasms* / diagnosis
  • Retroperitoneal Neoplasms* / diagnostic imaging
  • Retroperitoneal Neoplasms* / pathology
  • Retroperitoneal Neoplasms* / surgery
  • Time Factors
  • Tomography, X-Ray Computed
  • Ultrasonography, Doppler, Color
  • Vascular Neoplasms* / diagnosis
  • Vascular Neoplasms* / diagnostic imaging
  • Vascular Neoplasms* / pathology
  • Vascular Neoplasms* / surgery
  • Vena Cava, Inferior / pathology