The evolutionarily conserved interaction between LC3 and p62 selectively mediates autophagy-dependent degradation of mutant huntingtin

Cell Mol Neurobiol. 2010 Jul;30(5):795-806. doi: 10.1007/s10571-010-9507-y. Epub 2010 Mar 5.

Abstract

Mammalian p62/sequestosome-1 protein binds to both LC3, the mammalian homologue of yeast Atg8, and polyubiquitinated cargo proteins destined to undergo autophagy-mediated degradation. We previously identified a cargo receptor-binding domain in Atg8 that is essential for its interaction with the cargo receptor Atg19 in selective autophagic processes in yeast. We, thus, sought to determine whether this interaction is evolutionally conserved from yeast to mammals. Using an amino acid replacement approach, we demonstrate that cells expressing mutant LC3 (LC3-K30D, LC3-K51A, or LC3-L53A) all exhibit defective lipidation of LC3, a disrupted LC3-p62 interaction, and impaired autophagic degradation of p62, suggesting that the p62-binding site of LC3 is localized within an evolutionarily conserved domain. Importantly, whereas cells expressing these LC3 mutants exhibited similar overall autophagic activity comparable to that of cells expressing wild-type LC3, autophagy-mediated clearance of the aggregation-prone mutant Huntingtin was defective in the mutant-expressing cells. Together, these results suggest that p62 directly binds to the evolutionarily conserved cargo receptor-binding domain of Atg8/LC3 and selectively mediates the clearance of mutant Huntingtin.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing / metabolism*
  • Amino Acids, Basic / metabolism
  • Animals
  • Autophagy*
  • Cell Death
  • Cell Line
  • Evolution, Molecular*
  • Humans
  • Huntingtin Protein
  • Hydrophobic and Hydrophilic Interactions
  • Microtubule-Associated Proteins / metabolism*
  • Mutant Proteins / metabolism*
  • Mutation / genetics
  • Nerve Tissue Proteins / metabolism*
  • Nuclear Proteins / metabolism*
  • Phagosomes / metabolism
  • Protein Binding
  • Protein Processing, Post-Translational*
  • Protein Transport
  • Rats
  • Sequestosome-1 Protein
  • Structure-Activity Relationship
  • Ubiquitin / chemistry
  • Ubiquitin / metabolism

Substances

  • Adaptor Proteins, Signal Transducing
  • Amino Acids, Basic
  • HTT protein, human
  • Huntingtin Protein
  • LC3 protein, rat
  • Microtubule-Associated Proteins
  • Mutant Proteins
  • Nerve Tissue Proteins
  • Nuclear Proteins
  • SQSTM1 protein, human
  • Sequestosome-1 Protein
  • Ubiquitin