Paraganglioma-like dermal melanocytic tumor: a case report with particular features

Int J Clin Exp Pathol. 2009 Nov 20;3(2):222-5.

Abstract

Childhood dermal tumors with melanocytic features is an unusual tumor that can create diagnostic confusion. Among them, paraganglioma-like melanocytic tumors- previous included in melanocytic tumors of uncertain malignant potential- has some particular histopathologic and immunohistochemical features. We describe a case of 13 years old girl with a paraganglioma-like dermal melanocytic tumor of the left leg.

Keywords: Paraganglioma like dermal melanocytic lesion.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Antigens, Neoplasm / metabolism
  • Biopsy
  • Cell Lineage
  • Dermis / metabolism
  • Dermis / pathology*
  • Female
  • Humans
  • Immunohistochemistry / methods
  • MART-1 Antigen
  • Melanocytes / cytology
  • Melanoma / metabolism
  • Melanoma / pathology*
  • Melanoma / surgery
  • Neoplasm Proteins / metabolism
  • Paraganglioma / metabolism
  • Paraganglioma / pathology*
  • Paraganglioma / surgery
  • Proto-Oncogene Proteins c-kit / metabolism
  • S100 Proteins / metabolism
  • Skin Neoplasms / metabolism
  • Skin Neoplasms / pathology*
  • Skin Neoplasms / surgery
  • Vimentin / metabolism

Substances

  • Antigens, Neoplasm
  • MART-1 Antigen
  • MLANA protein, human
  • Neoplasm Proteins
  • S100 Proteins
  • Vimentin
  • Proto-Oncogene Proteins c-kit