Multiple gastrointestinal stromal tumors in a patient with type I neurofibromatosis presenting with tumor rupture and peritonitis

Ming-Chang Ku; Chung-Ming Tsai; Yeu-Sheng Tyan

doi:10.1016/j.clinimag.2009.03.005

Multiple gastrointestinal stromal tumors in a patient with type I neurofibromatosis presenting with tumor rupture and peritonitis

Clin Imaging. 2010 Jan-Feb;34(1):57-9. doi: 10.1016/j.clinimag.2009.03.005.

Authors

Ming-Chang Ku¹, Chung-Ming Tsai, Yeu-Sheng Tyan

Affiliation

¹ Department of Medical Imaging, Chun Shan Medical University Hospital, Taichung, Taiwan.

PMID: 20122521
DOI: 10.1016/j.clinimag.2009.03.005

Abstract

A young woman with type 1 neurofibromatosis (NF-1) complained of abdominal pain for 3 days. Computed tomography disclosed two jejunal tumors with rupture and peritonitis. Surgery revealed two tumors in the jejunum, one of which was ruptured. Specimen examination found four additional intramural nodules between these tumors. Histology proved these tumors were all gastrointestinal stromal tumors (GIST). The finding of multiple digestive tumors associated with peritonitis in an NF-1 patient should lead to the consideration of a ruptured GIST.

Publication types

Case Reports

MeSH terms

Adult
Female
Gastrointestinal Stromal Tumors / complications*
Gastrointestinal Stromal Tumors / diagnostic imaging*
Humans
Neoplasms, Multiple Primary / complications
Neoplasms, Multiple Primary / diagnostic imaging
Neurofibromatosis 1 / complications*
Neurofibromatosis 1 / diagnostic imaging*
Peritonitis / diagnostic imaging*
Peritonitis / etiology*
Radiography
Rupture, Spontaneous / complications
Rupture, Spontaneous / diagnostic imaging*