Overview of paediatric neuromuscular disorders and related pulmonary issues: diagnostic and therapeutic considerations

Paediatr Respir Rev. 2010 Mar;11(1):9-17. doi: 10.1016/j.prrv.2009.10.009. Epub 2009 Dec 5.

Abstract

Pulmonary compromise is common in neuromuscular disease. Respiratory failure may be a presenting feature of neuromuscular disease and remains a major cause of morbidity and mortality. This article will review the current understanding of the more commonly encountered neuromuscular disorders in childhood and emphasize related pulmonary issues.

Publication types

  • Review

MeSH terms

  • Child
  • Humans
  • Lung Diseases / etiology*
  • Neuromuscular Diseases / complications*
  • Respiratory Insufficiency / etiology*