Nutrition management of pediatric patients who have cystic fibrosis

Pediatr Clin North Am. 2009 Oct;56(5):1123-41. doi: 10.1016/j.pcl.2009.06.008.

Abstract

Since the identification of cystic fibrosis (CF) in the 1940s, nutrition care of patients who have CF has been a challenge. Through optimal caloric intake and careful management of malabsorption, patients are expected to meet genetic potential for growth. Yet factors beyond malabsorption, including nutrient activity at the cellular level, may influence growth and health. This article reviews nutrition topics frequently discussed in relationship to CF and presents intriguing new information describing nutrients currently being studied for their impact on overall health of patients who have CF.

Publication types

  • Review

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Choline / administration & dosage
  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / diet therapy
  • Cystic Fibrosis* / metabolism
  • Dietary Proteins / administration & dosage*
  • Energy Intake*
  • Fatty Acids, Essential / administration & dosage
  • Glutathione / administration & dosage
  • Humans
  • Infant
  • Malabsorption Syndromes / diagnosis
  • Malabsorption Syndromes / etiology
  • Malabsorption Syndromes / therapy*
  • Micronutrients / administration & dosage*
  • Minerals / administration & dosage
  • Trace Elements / administration & dosage
  • Ubiquinone / administration & dosage
  • Ubiquinone / analogs & derivatives
  • Vitamins / administration & dosage
  • Young Adult

Substances

  • Dietary Proteins
  • Fatty Acids, Essential
  • Micronutrients
  • Minerals
  • Trace Elements
  • Vitamins
  • Ubiquinone
  • coenzyme Q10
  • Glutathione
  • Choline