Simplified cell culture method for the diagnosis of atypical primary ciliary dyskinesia

Thorax. 2009 Dec;64(12):1077-81. doi: 10.1136/thx.2008.110940. Epub 2009 Sep 21.

Abstract

Background: The diagnosis of primary ciliary dyskinesia (PCD) can be challenging, and it may be particularly difficult to distinguish primary ciliary disease from the secondary changes after infections.

Objectives: The purpose of the study was to evaluate if nasal epithelial cells, obtained with nasal brushing instead of a biopsy, could be used in a culture system for the diagnosis of PCD in difficult cases.

Methods and main results: Ciliary motion analysis (CMA) and transmission electron microscopy (TEM) were performed on 59 subjects with persistent or recurrent pneumonia. These investigations allowed the diagnosis of PCD in 13 (22%) patients while the defect of the cilia was considered secondary to infections in 37 (63%) subjects. In the remaining nine (15%) patients the diagnostic evaluation with CMA and TEM remained inconclusive. Ciliogenesis in culture allowed the diagnosis of PCD in four of these patients, it was indicative of a secondary defect in two subjects, and it was not helpful in the remaining three patients.

Conclusions: Culture of cells obtained with brushing of the nasal turbinate is not a perfect test, nevertheless it may offer diagnostic help in doubtful cases of PCD.

Publication types

  • Evaluation Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Cell Culture Techniques / methods
  • Child
  • Child, Preschool
  • Cilia / ultrastructure
  • Ciliary Motility Disorders / diagnosis
  • Diagnosis, Differential
  • Female
  • Humans
  • Infant
  • Kartagener Syndrome / diagnosis*
  • Male
  • Middle Aged
  • Nasal Mucosa / pathology
  • Specimen Handling / methods
  • Young Adult