Objective: To identify an unusual histologic entity, extraovarian primary peritoneal carcinoma (EOPPC) along with a review of the recent literature.
Methods: A thorough clinical examination along with detail laboratory parameters was studied in a 56-year-old female who presented with ascites and an elevated serum CA-125. Multiple microscopic sections were studied from the surgical specimen received comprising of total hysterectomy, bilateral salpingo-oophorectomy and omentectomy.
Results: A diagnosis of EOPPC was made after a thorough study.
Conclusion: A correct diagnosis and timely management of this unusual histologic entity can result in long-term disease-free survival of the patient.