Cytolytic T cells induce ceramide-rich platforms in target cell membranes to initiate graft-versus-host disease

Blood. 2009 Oct 22;114(17):3693-706. doi: 10.1182/blood-2008-11-191148. Epub 2009 Aug 7.

Abstract

Alloreactive donor cytolytic T lymphocytes play a critical role in pathophysiology of acute graft-versus-host disease (GVHD). As GVHD progression involves tumor necrosis factor superfamily receptor activation, and as apoptotic signaling for some tumor necrosis factor superfamily receptors might involve acid sphingomyelinase (ASMase)-mediated ceramide generation, we hypothesized that ASMase deletion would ameliorate GVHD. Using clinically relevant mouse models of acute GVHD in which allogeneic bone marrow and T cells were transplanted into asmase+/+ and asmase(-/-) hosts, we identify host ASMase as critical for full-blown GVHD. Lack of host ASMase reduced the acute inflammatory phase of GVHD, attenuating cytokine storm, CD8+ T-cell proliferation/activation, and apoptosis of relevant graft-versus-host target cells (hepatocytes, intestinal, and skin cells). Organ injury was diminished in asmase(-/-) hosts, and morbidity and mortality improved at 90 days after transplantation. Resistance to cytolytic T lymphocyte-induced apoptosis was found at the target cell membrane if hepatocytes lack ASMase, as hepatocyte apoptosis required target cell ceramide generation for formation of ceramide-rich macrodomains, sites concentrating proapoptotic Fas. These studies indicate a requirement for target cell ASMase in evolution of GVHD in liver, small intestines, and skin and provide potential new targets for disease management.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis / immunology*
  • Bone Marrow Transplantation
  • CD8-Positive T-Lymphocytes / immunology*
  • Cell Membrane / immunology*
  • Cell Membrane / metabolism
  • Cell Membrane / pathology
  • Ceramides / immunology*
  • Cytokines / metabolism
  • Disease Models, Animal
  • Female
  • Graft vs Host Disease / immunology*
  • Graft vs Host Disease / mortality
  • Graft vs Host Disease / pathology
  • Hepatocytes / immunology
  • Hepatocytes / metabolism
  • Interferon-gamma / metabolism
  • Intestine, Small / cytology
  • Intestine, Small / immunology
  • Intestine, Small / metabolism
  • Liver / cytology
  • Liver / immunology
  • Liver / metabolism
  • Lymphocyte Activation
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Inbred MRL lpr
  • Mice, SCID
  • Skin / cytology
  • Skin / immunology
  • Skin / metabolism
  • Sphingomyelin Phosphodiesterase / physiology*
  • Survival Rate
  • T-Lymphocytes, Cytotoxic / immunology*

Substances

  • Ceramides
  • Cytokines
  • Interferon-gamma
  • acid sphingomyelinase-1
  • Sphingomyelin Phosphodiesterase