Testicular feminization with persistent wolffian duct and müllerian remnants: similar to Mayer-Rokitansky-Kuster-Hauser syndrome

Fertil Steril. 2009 Dec;92(6):2034-6. doi: 10.1016/j.fertnstert.2008.12.126. Epub 2009 May 6.

Abstract

Testicular feminization findings in a 24-year-old woman closely resembled those of Mayer-Rokitansky-Kuster-Hauser syndrome with persistent müllerian remnants and wolffian duct regression.

Publication types

  • Case Reports

MeSH terms

  • Androgen-Insensitivity Syndrome / pathology*
  • Female
  • Feminization / pathology*
  • Humans
  • Laparoscopy
  • Male
  • Mullerian Ducts / abnormalities*
  • Testis / abnormalities*
  • Uterus / abnormalities
  • Vagina / abnormalities
  • Wolffian Ducts / abnormalities*
  • Young Adult