Fibrous dysplasia of the maxilla

J Pediatr Surg. 2009 Apr;44(4):849-51. doi: 10.1016/j.jpedsurg.2008.12.006.

Abstract

Fibrous dysplasia is a rare disorder of the bone. It is seen in 2 main forms of presentation, monoostotic and the polyostotic form with café au lait spots and precocious puberty (McCune-Albright syndrome). Most of the cases present in the first 2 decades of life, and the lesions are rare in infants (Joseph E, Kachara R, Bhattacharya RN, et al. Fibrous dysplasia of the orbit in an infant. Pediatr Neurosurg 2000; 32: 205-208). Herein, we present a rare case of fibrous dysplasia in an infant.

Publication types

  • Case Reports

MeSH terms

  • Biopsy, Needle
  • Fibrous Dysplasia of Bone / diagnosis
  • Fibrous Dysplasia of Bone / pathology*
  • Fibrous Dysplasia of Bone / surgery*
  • Follow-Up Studies
  • Humans
  • Immunohistochemistry
  • Infant
  • Magnetic Resonance Imaging
  • Male
  • Maxilla / pathology*
  • Maxilla / surgery*
  • Postoperative Care / methods
  • Rare Diseases
  • Surgical Procedures, Operative / methods
  • Tomography, X-Ray Computed
  • Treatment Outcome