Survival into sixth decade of untreated pulmonary atresia with ventricular septal defect and major aorto-pulmonary collaterals: a magnetic resonance imaging study

J Cardiovasc Med (Hagerstown). 2009 Jul;10(7):570-1. doi: 10.2459/JCM.0b013e32832b4b36.

Abstract

A 56-year-old male with a history of untreated pulmonary atresia with ventricular septal defect diagnosed during childhood was referred to our institution for congestive heart failure. We describe the MR imaging findings that documented the presence of multiple aorto-pulmonary collaterals arising from the abdominal aorta and from the internal mammary artery supplying both pulmonary arteries. This is the oldest known surviving case documented in medical literature.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / pathology*
  • Abnormalities, Multiple / physiopathology
  • Age Factors
  • Aorta, Abdominal / pathology*
  • Aorta, Abdominal / physiopathology
  • Collateral Circulation*
  • Heart Failure / etiology
  • Heart Failure / pathology*
  • Heart Failure / physiopathology
  • Heart Septal Defects, Ventricular / complications
  • Heart Septal Defects, Ventricular / pathology*
  • Heart Septal Defects, Ventricular / physiopathology
  • Humans
  • Magnetic Resonance Angiography*
  • Magnetic Resonance Imaging, Cine*
  • Male
  • Mammary Arteries / pathology
  • Mammary Arteries / physiopathology
  • Middle Aged
  • Pulmonary Artery / pathology*
  • Pulmonary Artery / physiopathology
  • Pulmonary Atresia / complications
  • Pulmonary Atresia / pathology*
  • Pulmonary Atresia / physiopathology
  • Pulmonary Circulation
  • Regional Blood Flow