Epidermolysis bullosa acquisita (EBA) and esophageal webs: a new association

Am J Gastroenterol. 1991 Oct;86(10):1518-22.

Abstract

Epidermolysis bullosa acquisita (EBA) is a well-defined, blistering disorder of the skin associated with autoantibodies to type VII collagen. Although esophageal pathology is common in children with hereditary dystrophic forms of epidermolysis bullosa, esophageal problems have not been reported previously in patients with bona fide EBA. In this report, a 71-yr-old white female with longstanding EBA presented with recurrent dysphagia and multiple esophageal webs that responded to esophageal dilatation.

Publication types

  • Case Reports
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Aged
  • Deglutition Disorders / etiology
  • Epidermolysis Bullosa Acquisita / complications*
  • Epidermolysis Bullosa Acquisita / pathology
  • Esophageal Diseases / complications*
  • Esophageal Diseases / diagnostic imaging
  • Esophageal Diseases / pathology
  • Female
  • Humans
  • Radiography