Abnormally thickened papillary muscle resulting in dynamic left ventricular outflow tract obstruction: an unusual presentation of hypertrophic cardiomyopathy

Bethany A Austin; Deborah H Kwon; Nicholas G Smedira; Maran Thamilarasan; Harry M Lever; Milind Y Desai

doi:10.1016/j.echo.2008.10.022

Abnormally thickened papillary muscle resulting in dynamic left ventricular outflow tract obstruction: an unusual presentation of hypertrophic cardiomyopathy

J Am Soc Echocardiogr. 2009 Jan;22(1):105.e5-6. doi: 10.1016/j.echo.2008.10.022.

Authors

Bethany A Austin¹, Deborah H Kwon, Nicholas G Smedira, Maran Thamilarasan, Harry M Lever, Milind Y Desai

Affiliation

¹ Department of Cardiovascular Medicine, Heart and Vascular Institute, Cleveland Clinic, Cleveland, OH 44195, USA.

PMID: 19131012
DOI: 10.1016/j.echo.2008.10.022

Abstract

We report the case of a symptomatic 18-year-old patient, gene-positive for hypertrophic cardiomyopathy (HCM), who presented with symptomatic dynamic left ventricular outflow tract (LVOT) obstruction caused by an abnormally thickened papillary muscle in the absence of septal hypertrophy. This was confirmed using multimodality imaging, including echocardiography and magnetic resonance imaging. He successfully underwent surgery for papillary muscle realignment without septal myectomy.

Publication types

Case Reports

MeSH terms

Cardiomyopathies / complications*
Cardiomyopathies / diagnostic imaging*
Cardiomyopathy, Hypertrophic / complications*
Cardiomyopathy, Hypertrophic / diagnostic imaging*
Humans
Male
Papillary Muscles / diagnostic imaging*
Rare Diseases
Ultrasonography
Ventricular Outflow Obstruction / complications*
Ventricular Outflow Obstruction / diagnostic imaging*