Whipple's procedure in a renal transplant recipient with polycystic liver disease

JOP. 2008 Jul 10;9(4):515-9.

Abstract

Context: Polycystic disease is a rare disorder, which most commonly manifests in the kidney and liver. Recently an increased risk for pancreatic malignancies in subsets of patients with polycystic disease has been reported.

Case report: We report a patient with polycystic liver and kidney disease who successfully underwent a Whipple's procedure for pancreatic adenocarcinoma.

Conclusion: Although technical difficulty may increase, pancreaticoduodenectomy can be safely performed in patients with polycystic liver disease.

Publication types

  • Case Reports

MeSH terms

  • Adenocarcinoma / diagnosis
  • Adenocarcinoma / diagnostic imaging
  • Adenocarcinoma / surgery*
  • Aged
  • Cholangiopancreatography, Endoscopic Retrograde
  • Cysts / complications*
  • Cysts / diagnostic imaging
  • Fatal Outcome
  • Female
  • Fluorodeoxyglucose F18
  • Humans
  • Kidney Transplantation*
  • Liver Diseases / complications*
  • Liver Diseases / diagnostic imaging
  • Pancreatic Neoplasms / diagnosis
  • Pancreatic Neoplasms / diagnostic imaging
  • Pancreatic Neoplasms / surgery*
  • Pancreaticoduodenectomy*
  • Polycystic Kidney Diseases / complications*
  • Polycystic Kidney Diseases / surgery
  • Positron-Emission Tomography

Substances

  • Fluorodeoxyglucose F18