Non-vascular vision loss in pseudoxanthoma elasticum

Doc Ophthalmol. 2008 Jul;117(1):65-7. doi: 10.1007/s10633-007-9100-y. Epub 2007 Nov 22.

Abstract

Pseudoxanthoma elasticum patients with angioid streaks are well-known to have acute vision loss due to choroidal bleeding. However, chronic vision loss due to macular atrophy is less well characterized. We describe a patient with sub-acute vision loss in one eye due to loss of macular retinal pigment epithelium function. Autofluorescence and pattern electroretinogram were useful adjuncts to help diagnose the source of her vision loss.

Publication types

  • Case Reports
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Angioid Streaks / complications
  • Angioid Streaks / diagnosis
  • Atrophy
  • Electroretinography
  • Female
  • Fluorescein Angiography
  • Humans
  • Pigment Epithelium of Eye / pathology*
  • Pseudoxanthoma Elasticum / complications*
  • Pseudoxanthoma Elasticum / diagnosis
  • Vision Disorders / diagnosis
  • Vision Disorders / etiology*
  • Visual Acuity