We report on a case of rhabdomyosarcoma of the bladder in an adult patient. A 65-year-old woman presented with macroscopic hematuria. Ultrasonography revealed a large bladder tumor and severe hydronephrosis of the right kidney. Computed tomography (CT) confirmed these findings and revealed extravesical tumor extension. Cystoscopic biopsy of the tumor showed botryoid rhabdomyo- sarcoma. The patient's local and general conditions did not allow any adjuvant treatment. The patient died of disease 6 months later.