Flatiron mice and ferroportin disease

Nutr Rev. 2007 Jul;65(7):341-5. doi: 10.1111/j.1753-4887.2007.tb00312.x.

Abstract

Flatiron mice provide the first genetic model that fully recapitulates the iron-loading disorder ferroportin disease. Unlike the other known genetic causes of hemochromatosis, missense mutations in the ferroportin gene are autosomal dominant. These new findings show that ferroportin disease results from dominant negative effects rather than haplo-insufficiency.

Publication types

  • Review

MeSH terms

  • Animals
  • Animals, Genetically Modified*
  • Cation Transport Proteins / genetics*
  • Disease Models, Animal
  • Genes, Dominant
  • Hemochromatosis / genetics*
  • Humans
  • Iron / metabolism
  • Iron Metabolism Disorders / genetics*
  • Mice
  • Mice, Mutant Strains*
  • Mutation

Substances

  • Cation Transport Proteins
  • metal transporting protein 1
  • Iron