Unusual acute onset of pedunculated extragastric leiomyosarcoma. Case report

G Chir. 2007 Jun-Jul;28(6-7):265-9.

Abstract

Introduction: A case report of 25 yrs-old man with pedunculated exogastric leiomyosarcoma (with acute onset) surgically treated is presented.

Case report: The patient was operated after clinical, instrumental and blood sample tests. We performed a 5 cm wedge resection of the stomach in continuity with the omentum. Careful inspection revealed neither adenopathy nor metastases.

Results: Actual complete remission of pathology. Negative 1 year follow up by endoscopy and CT.

Discussion: Information on gastric leiomyosarcoma (LM), such as prognostic factors, patterns of disease recurrence, and optimal methods of treatment, are derived from limited clinical experience. Although about 25% of the gastric mesenchymal tumors present an exogastric growth, pedunculated exogastric leiomyosarcomas are extremely rare. Lymphatic spread of gastric LM is uncommon, therefore a formal lymph node dissection is not standard surgical management. At present, there is no evidence of intraperitoneal seeding from exogastric leiomyosarcomas. Consequently, a local resection with an adequate margin is sufficient when no invasion to the adjacent structures is observed. Neither the addition of lymphadenectomy nor the wider tumor-free margins of a radical gastrectomy seemed superior to the more conservative local excision.

Conclusions: Further studies are called for to elucidate if exogastric tumours lead to peritoneal seeding and, thereby, affect tumour survival.

Publication types

  • Case Reports

MeSH terms

  • Acute Disease
  • Adult
  • Humans
  • Leiomyosarcoma / pathology
  • Leiomyosarcoma / surgery*
  • Male
  • Stomach Neoplasms / pathology
  • Stomach Neoplasms / secondary*
  • Stomach Neoplasms / surgery*