Rapid aneurysmal degeneration of a Stanford type B aortic dissection in a patient with Loeys-Dietz syndrome

J Thorac Cardiovasc Surg. 2007 Jul;134(1):242-3, 243.e1. doi: 10.1016/j.jtcvs.2007.03.004.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / genetics*
  • Adult
  • Aortic Aneurysm / diagnosis*
  • Aortic Aneurysm / genetics*
  • Aortic Aneurysm / surgery
  • Aortic Dissection / diagnosis*
  • Aortic Dissection / genetics*
  • Aortic Dissection / surgery
  • Female
  • Humans
  • Mutation, Missense*
  • Protein Serine-Threonine Kinases
  • Receptor, Transforming Growth Factor-beta Type II
  • Receptors, Transforming Growth Factor beta / genetics*
  • Syndrome

Substances

  • Receptors, Transforming Growth Factor beta
  • Protein Serine-Threonine Kinases
  • Receptor, Transforming Growth Factor-beta Type II