We report the case of a child with unilateral linear scleroderma disturbing the right lower limb. It took three-quarters of a year to be diagnosed as linear scleroderma and another 8 months to be treated with oral steroids. Although functional disabilities of the right knee and foot were improved with the steroid therapy, the limb asymmetry has remained. We believe that early treatment with steroids is essential for childhood linear scleroderma with lesions over any joints.