Abstract
X-linked agammaglobulinemia (XLA) is a primary immune deficiency disease with a B-cell defect. We present the first XLA patient who had recurrent Campylobacter lari bacteremia. High dose intravenous immunoglobulin combined with azithromycin once per week, and a complete avoidance of bacterial reservoirs may be helpful for the prevention of C. lari bacteremia.
MeSH terms
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Adolescent
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Agammaglobulinemia / complications*
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Agammaglobulinemia / microbiology
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Azithromycin / therapeutic use
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Bacteremia / drug therapy
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Bacteremia / etiology*
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Campylobacter lari*
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Drug Therapy, Combination
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Genetic Diseases, X-Linked / complications*
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Genetic Diseases, X-Linked / microbiology
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Humans
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Immunoglobulins, Intravenous / therapeutic use
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Male
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Recurrence
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Sinusitis / etiology
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Sinusitis / microbiology
Substances
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Immunoglobulins, Intravenous
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Azithromycin