Elejalde syndrome--a case report

Am J Med Genet A. 2006 Oct 15;140(20):2223-6. doi: 10.1002/ajmg.a.31419.

Abstract

Elejalde syndrome (McKusick 200995), also known as acrocephalopolydactylous dysplasia, is a rare condition. We describe a sixth patient with this syndrome which is characterized by craniosynostosis and hyperproliferation of fibroblasts in many tissues including skin, liver, kidney, and pancreas. The cause of the syndrome is the homozygous state of an autosomal recessive mutation. We present a hypothesis that Elejalde syndrome might be associated with an inactivating FGFR gene mutation.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Abnormalities, Multiple / diagnostic imaging
  • Abnormalities, Multiple / genetics*
  • Abnormalities, Multiple / pathology*
  • Craniosynostoses / diagnostic imaging
  • Craniosynostoses / genetics*
  • Craniosynostoses / pathology*
  • Female
  • Humans
  • Infant, Newborn
  • Kidney / pathology
  • Liver / pathology
  • Pancreas / pathology
  • Radiography
  • Skin / pathology
  • Syndrome