Objective: Lymphangiomas are lesions usually presenting during childhood and are located mainly in the head and neck region; less than 5% are intraabdominal. Lymphangiomatosis is the term used for multifocal or diffuse lymphangiomas.
Methods and results: We report the case of a mesenteric lymphangiomatosis presenting as an acute abdomen in a 19-year-old man, review the literature and discuss the clinical management of these patients.
Conclusions: Prognosis and treatment of these lesions depends of its site of origin and extension, being complete surgical excision the optimal treatment.