Craniofacial surgery in fibrous dysplasia

J Pediatr Endocrinol Metab. 2006 May:19 Suppl 2:595-604. doi: 10.1515/jpem.2006.19.s2.595.

Abstract

Cranio-orbital fibrous dysplasia usually causes proptosis, visual loss, ocular motility impairment and cosmetic deformity. The goals of cranial fibrous dysplasia management are to preserve neurological functions and improve cosmesis. Strict neurological and ophthalmological follow-up and early cranio-facial surgery enables non-aggressive treatment without significant morbidity. Furthermore, good results are achieved thanks to new techniques and materials especially in children and adolescents. The aim of the present paper is to discuss surgical indications, techniques and outcomes of cranio-facial-orbital fibrous dysplasia on the basis of personal experience of 14 patients who underwent surgery.

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Craniofacial Abnormalities / etiology
  • Craniofacial Abnormalities / surgery*
  • Exophthalmos / etiology
  • Exophthalmos / surgery
  • Female
  • Fibrous Dysplasia of Bone / complications
  • Fibrous Dysplasia of Bone / surgery*
  • Humans
  • Male
  • Middle Aged
  • Orbit / pathology
  • Orbit / surgery
  • Orbital Diseases / etiology
  • Orbital Diseases / surgery*
  • Plastic Surgery Procedures / methods*
  • Retrospective Studies
  • Skull / pathology
  • Skull / surgery*
  • Treatment Outcome