Abstract
The authors review the immunopathology of invasive pneumococcal infections in patients with primary immunodeficiency diseases, with particular emphasis on selective anti-polysaccharide antibody deficiency. They summarize current knowledge on the molecular mechanisms and clinical manifestations of host defense against Str. pneumoniae.
MeSH terms
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Antibodies, Bacterial / metabolism*
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B-Lymphocytes / immunology
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Complement System Proteins / deficiency
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Humans
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Immunocompromised Host*
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Immunologic Deficiency Syndromes / complications*
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Immunologic Deficiency Syndromes / immunology*
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Phagocytes / immunology
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Pneumococcal Infections / etiology*
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Pneumococcal Infections / immunology
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Pneumococcal Infections / microbiology
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Pneumococcal Infections / virology
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Polysaccharides, Bacterial / immunology*
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Streptococcus pneumoniae
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T-Lymphocytes / immunology
Substances
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Antibodies, Bacterial
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Polysaccharides, Bacterial
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Complement System Proteins