Abstract
Three cases of trichoepithelioma associated with cylindroma (Brooke-Spiegler syndrome) in the same family are reported. Three generations were affected. The syndrome usually beginning at puberty is inherited as an irregular autosomal dominant trait.
MeSH terms
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Adult
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Aged
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Carcinoma, Adenoid Cystic / complications
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Carcinoma, Adenoid Cystic / genetics
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Carcinoma, Adenoid Cystic / pathology*
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Facial Neoplasms / complications
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Facial Neoplasms / genetics
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Facial Neoplasms / pathology*
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Female
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Genes, Dominant
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Humans
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Neoplastic Syndromes, Hereditary / complications
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Neoplastic Syndromes, Hereditary / genetics
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Neoplastic Syndromes, Hereditary / pathology*
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Pedigree
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Terminology as Topic