Ovarian adrenal rest tissue in congenital adrenal hyperplasia--a patient report

J Pediatr Endocrinol Metab. 2006 Feb;19(2):177-82. doi: 10.1515/jpem.2006.19.2.177.

Abstract

We report a young girl who died in an Addisonian crisis due to previously undiagnosed congenital adrenal hyperplasia (CAH), in whom ovarian adrenal rest tissue was detected at postmortem histopathological examination. This is a very rare complication in female patients with CAH with only two previously reported cases.

Publication types

  • Case Reports

MeSH terms

  • Addison Disease / complications*
  • Addison Disease / pathology
  • Adrenal Hyperplasia, Congenital / complications*
  • Adrenal Hyperplasia, Congenital / pathology
  • Adrenal Rest Tumor / complications*
  • Adrenal Rest Tumor / pathology
  • Fatal Outcome
  • Female
  • Humans
  • Infant
  • Ovarian Neoplasms / complications*
  • Ovarian Neoplasms / pathology