Type II mixed cryoglobulinaemia as an oligo rather than a mono B-cell disorder: evidence from GeneScan and MALDI-TOF analyses

Rheumatology (Oxford). 2006 Jun;45(6):685-93. doi: 10.1093/rheumatology/kei278. Epub 2006 Jan 6.

Abstract

Objective: To identify and characterize rheumatoid factor (RF)-producing B-cells and cryoprecipitate immunoglobulin (Ig) M in hepatitis C virus (HCV)-positive patients.

Methods: We purified and characterized, by peptide mass fingerprinting integrated with an NCBI IgBlast data bank search, the IgM component of cryoprecipitate and analysed the VDJ pattern of bone marrow B-cells by gene scan analysis of 17 HCV-positive patients with type II mixed-cryoglobulinaemia.

Results: IgM purified from all of the patients presented an RF specificity. In three of these patients a high and predominant B-cell clone (>or=30%) was found in the bone marrow. B-cell-receptor sequences were determined and immunophenotyping of these clones was performed. Peptide masses originating after tryptic digestion of the B-cell-receptor combinatory regions and those originating by tryptic digestion of the cryoprecipitated IgM from the same patient were comparable. In the remaining patients an oligoclonal/polyclonality was found. However, in some of these patients we were able to find peptides that matched with the B-cell-receptor sequences of overexpanded B cells, indicating that, even in the absence of a clear monoclonal expansion, a fraction of total cryoprecipated IgM may derive from overexpanded B-cell clones found in patients' bone marrow.

Conclusions: In the majority of mixed cryoglobulinaemia-HCV-positive patients, both in the serum and in B cells from the bone marrow, an oligoclonal pattern is the main molecular picture. When a monoclonal B-cell clone is found, its B-cell-receptor shows an antigen-binding fragment identical to that of cryoprecipitable RF-IgM. Phenotypically, B cells are CD20-positive but CD5-negative, suggesting that the B-1 B-cell subset is not likely to produce high-affinity IgM-RF molecules.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Amino Acid Sequence
  • B-Lymphocytes / immunology*
  • B-Lymphocytes / pathology
  • Bone Marrow Cells / immunology
  • Clone Cells / immunology
  • Clone Cells / pathology
  • Cryoglobulinemia / genetics
  • Cryoglobulinemia / immunology*
  • Cryoglobulinemia / virology
  • Female
  • Genes, Immunoglobulin
  • Hepatitis C / complications
  • Hepatitis C / immunology
  • Humans
  • Immunoglobulin Heavy Chains / genetics
  • Immunoglobulin Light Chains / genetics
  • Immunoglobulin M / genetics
  • Immunoglobulin M / immunology
  • Immunophenotyping
  • Male
  • Middle Aged
  • Molecular Sequence Data
  • Mutation
  • Rheumatoid Factor / immunology
  • Spectrometry, Mass, Matrix-Assisted Laser Desorption-Ionization

Substances

  • Immunoglobulin Heavy Chains
  • Immunoglobulin Light Chains
  • Immunoglobulin M
  • Rheumatoid Factor